Nevus comedonicus is an uncommon skin abnormality first described in 1895 by Kofmann who used the term “comedo nevus.” It comprises of groups of pits filled with black keratinous plugs resembling blackheads, with inflammatory acne lesions developing later. Nevus comedonicus is caused by a defect in the development of the hair follicle. Lesions may develop any time from birth to middle age, but are usually present at birth or develop before the age of 10 years. Men and women are equally affected. There is no racial predilection.